Abstract
Factor X deficiency is a rare, autosomal recessive disorder that involves the
coagulation cascade. People with this disorder present with a myriad of early life
bleeding complications. We report here a 23-year-old male, who presented
with bleeding complications (prolonged bleeding from surgical wounds,
unresolving hematomas, uncontrolled nasal bleeding, hematuria and
hematochezia) at different stages of his life but was diagnosed very late for
factor X deficiency after comprehensive evaluation for clotting factors. He was
managed by repeated transfusions of fresh frozen plasma and detailed
counselling. Factor X deficiency is a rare life-threatening disease and must be
differentiated from other disorders of coagulation. The patients are advised to
avoid activities with high levels of physical contact, unnecessary invasive
interventions and drugs that remarkably affect liver functions and seek
immediate medical care in case of bleeding from any site.
Fatima Ayaz, Saeed Bin Ayaz, Muhammad Furrukh. (2018) FACTOR-X DEFICIENCY: A RARE DISORDERTO BE LOOKED FOR IN CASES OFCONGENITAL BLEEDING TENDENCY, KHYBER MEDICAL UNIVERSITY JOURNAL, Volume 10, Issue 3.
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