Abstract
Ewing sarcoma causing unilateral proptosis in a child is unusual presentation. Ayoung girl presented with painless proptosis of left eye with restricted eyemovements. Her radiology revealed a large soft tissue mass causing destructionof lateral orbital wall and zygomatic arch measuring 2.0 × 3.0 cm. Total excisionof intracranial and intra orbital part of the tumor brought about substantial relief.The clinical and radiological presentation and management of this entity arediscussed.Key words: Sphenoid bone, Ewing sarcoma, orbital proptosis, primitiveneuroepithelial tumor (PNET), radiology, small round cell tumor, surgery.
